Protein Details: Calcium-activated chloride channel regulator 1

Protein ID

ICDB_Pro_0068

Protein Name

Calcium-activated chloride channel regulator 1

Gene Name

CLCA1; CACC1

Organism

Homo sapiens (Human)

Length

914 amino acids

AlphaFoldDB

AF-A8K7I4-F1-model_v4.pdb

Function

May be involved in mediating calcium-activated chloride conductance. May play critical roles in goblet cell metaplasia; mucus hypersecretion; cystic fibrosis and AHR. May be involved in the regulation of mucus production and/or secretion by goblet cells. Involved in the regulation of tissue inflammation in the innate immune response. May play a role as a tumor suppressor. Induces MUC5AC.

Sequence

MGPFKSSVFILILHLLEGALSNSLIQLNNNGYEGIVVAIDPNVPEDETLIQQIKDMVTQASLYLLEATGKRFYFKNVAILIPETWKTKADYVRPKLETYKNADVLVAESTPPGNDEPYTEQMGNCGEKGERIHLTPDFIAGKKLAEYGPQGRAFVHEWAHLRWGVFDEYNNDEKFYLSNGRIQAVRCSAGITGTNVVKKCQGGSCYTKRCTFNKVTGLYEKGCEFVLQSRQTEKASIMFAQHVDSIVEFCTEQNHNKEAPNKQNQKCNLRSTWEVIRDSEDFKKTTPMTTQPPNPTFSLLQIGQRIVCLVLDKSGSMATGNRLNRLNQAGQLFLLQTVELGSWVGMVTFDSAAHVQNELIQINSGSDRDTLAKRLPAAASGGTSICSGLRSAFTVIRKKYPTDGSEIVLLTDGEDNTISGCFNEVKQSGAIIHTVALGPSAAQELEELSKMTGGLQTYASDQVQNNGLIDAFGALSSGNGAVSQRSIQLESKGLTLQNSQWMNGTVIVDSTVGKDTLFLITWTMQPPQILLWDPSGQKQGGFVVDKNTKMAYLQIPGIAKVGTWKYSLQASSQTLTLTVTSRASNATLPPITVTSKTNKDTSKFPSPLVVYANIRQGASPILRASVTALIESVNGKTVTLELLDNGAGADATKDDGVYSRYFTTYDTNGRYSVKVRALGGVNAARRRVIPQQSGALYIPGWIENDEIQWNPPRPEINKDDVQHKQVCFSRTSSGGSFVASDVPNAPIPDLFPPGQITDLKAEIHGGSLINLTWTAPGDDYDHGTAHKYIIRISTSILDLRDKFNESLQVNTTALIPKEANSEEVFLFKPENITFENGTDLFIAIQAVDKVDLKSEISNIARVSLFIPPQTPPETPSPDETSAPCPNIHINSTIPGIHILKIMWKWIGELQLSIA

PDB Structures

Ligand Binding

1. DICL_CP

2. DICL_Pep

Binding Site

BINDING 156; /ligand="Zn(2+)"; /ligand_note="catalytic"; BINDING 160; /ligand="Zn(2+)"; /ligand_note="catalytic"; BINDING 167; /ligand="Zn(2+)"; /ligand_note="catalytic";

Disease

Pontocerebellar Hypoplasia;Type 8 and Cystic Fibrosis

Location

Highly expressed in small intestine and colon namely in intestinal basal crypt epithelia and goblet cells; and appendix. Weakly expressed in uterus; testis and kidney. Expressed in the airways epithelium of both asthmatic and healthy patients. Expressed in the airways epithelium of both asthmatic and healthy patients. Expressed in the airways epithelium of both asthmatic and healthy patients. Expressed in the bronchial epithelium; especially in mucus-producing goblet cells. Expressed in normal turbinate mucosa and nasal polyp. Expressed in.

DOI ID

10.1006/geno.1998.5562; 10.1016/s0014-5793(99)00891-1; 10.1038/ng1285; 10.1038/nature04727; 10.1074/jbc.m112.410282; 10.1089/10445490152122442; 10.1164/ajrccm.165.8.2107068; 10.1067/mai.2002.121555; 10.1080/00016480510028519; 10.1016/j.jaci.2004.09.039; 10.1074/jbc.m504654200; 10.1165/rcmb.2004-0220rc; 10.1159/000104419

RefSeq

NP_001276.2

Feature